Though developmental anomalies of the sound conducting apparatus are not so very common, surgical correction techniques have been used such as auricular reconstruction cancal prosthesis, tympanoplasty, penestration operation because of the being impairment from birth which, if bilateral, may be sufficient to interfere with the normal development of speech and also affect with normal personality acquire when external deformity accompanies. The optimum age of correction is not identical for bilateral and unilateral, and the results of surgery are accordingly to the cochler fuction, pneumatization, grade of anomaly and its shape. Author report a case of 7-year old girl patient who had congenital anomalies similar with Treacher-Collins symdrome with the available examination and references.